Ectopic Sinonasal Adamantinomatous Craniopharyngioma in an Adolescent.

Abstract

Craniopharyngiomas are uncommon benign intracranial tumours with aggressive behaviour predominantly seen in the suprasellar region. Two distinct subtypes have been identified: adamantinomatous, usually seen in childhood, and papillary, most often found in middle-aged adults. We describe a rare adamantinomatous craniopharyngioma in the sinonasal region with intraorbital extension in an adolescent female who presented with chronic left-sided nasal blockage and left eye proptosis. The tumour was successfully resected via an endonasal transsphenoidal approach, and no residual tumour was found in post-operative imaging. Clinicians must consider this disease as a possible differential diagnosis in the presence of a sinonasal mass. Early recognition of sinonasal craniopharyngioma enables prompt treatment that can minimise its associated long-term morbidities and achieve disease-free status.