Kaposiform Hemangioendothelioma with Kasabach-Merritt Phenomenon: A Rare Diagnosis of Neck Mass in a Child.

IF 0.4 Q4 SURGERY

Indian Journal of Otolaryngology and Head and Neck Surgery Pub Date : 2025-08-01 Epub Date: 2025-06-04 DOI:10.1007/s12070-025-05620-3

Anis Che Mohd Amin, Najwa Raihan Zulkiflee, Azliana Aziz, Hashimah Ismail

引用次数: 0

Abstract

Kaposiform hemangioendothelioma (KHE) is a rare aggressive vascular tumour of intermediate malignant potential and often associated with thrombocytopaenia, known as the Kasabach-Merritt phenomenon (KMP). Herein, we report a case of a 3-month-old child with a left neck mass, subsequently diagnosed with KHE, complicated with KMP. This case was managed with a multidisciplinary team involvement and successfully treated with the combination of steroids and sirolimus. As the diagnosis of KHE itself is rare, one may miss the differential diagnosis causing a delay in referral and subsequently late in diagnosis and initiating the treatment.

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卡泊西样血管内皮瘤伴卡萨巴赫-梅里特现象：儿童颈部肿块的罕见诊断。

卡波西样血管内皮瘤（KHE）是一种罕见的侵袭性血管肿瘤，具有中等恶性潜能，常伴有血小板减少症，称为卡萨巴赫-梅里特现象（KMP）。在此，我们报告一个3个月大的婴儿左颈部肿块，随后被诊断为KHE，并发KMP。该病例由多学科团队参与管理，并成功地使用类固醇和西罗莫司联合治疗。由于KHE本身的诊断是罕见的，人们可能会错过鉴别诊断，导致延误转诊，随后诊断和开始治疗。

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来源期刊

Indian Journal of Otolaryngology and Head and Neck Surgery Medicine-Otorhinolaryngology

CiteScore

0.80

自引率

0.00%

发文量

226

审稿时长

6-12 weeks

期刊介绍： Indian Journal of Otolaryngology and Head & Neck Surgery was founded as Indian Journal of Otolaryngology in 1949 as a scientific Journal published by the Association of Otolaryngologists of India and was later rechristened as IJOHNS to incorporate the changes and progress. IJOHNS, undoubtedly one of the oldest Journals in India, is the official publication of the Association of Otolaryngologists of India and is about to publish it is 67th Volume in 2015. The Journal published quarterly accepts articles in general Oto-Rhino-Laryngology and various subspecialities such as Otology, Rhinology, Laryngology and Phonosurgery, Neurotology, Head and Neck Surgery etc. The Journal acts as a window to showcase and project the clinical and research work done by Otolaryngologists community in India and around the world. It is a continued source of useful clinical information with peer review by eminent Otolaryngologists of repute in their respective fields. The Journal accepts articles pertaining to clinical reports, Clinical studies, Research articles in basic and applied Otolaryngology, short Communications, Clinical records reporting unusual presentations or lesions and new surgical techniques. The journal acts as a catalyst and mirrors the Indian Otolaryngologist’s active interests and pursuits. The Journal also invites articles from senior and experienced authors on interesting topics in Otolaryngology and allied sciences from all over the world. The print version is distributed free to about 4000 members of Association of Otolaryngologists of India and the e-Journal shortly going to make its appearance on the Springer Board can be accessed by all the members. Association of Otolaryngologists of India and M/s Springer India group have come together to co-publish IJOHNS from January 2007 and this bondage is going to provide an impetus to the Journal in terms of international presence and global exposure.