Supracardiac total anomalous pulmonary venous drainage with right-sided vertical vein draining into the proximal superior vena cava.

Abstract

Total anomalous pulmonary venous drainage (TAPVC) is a rare congenital anomaly with drainage of all the pulmonary veins into the systemic circulation instead of the left atrium. The commonest anomalous pattern of supracardiac TAPVC includes formation of the left-sided vertical vein draining into the left brachiocephalic vein. All the pulmonary veins forming a right-sided vertical vein and draining into proximal superior vena cava (SVC) are a highly uncommon variant, with distinct anatomical course. We present an extremely rare case of an 8-month-old child who presented with a variant pattern of drainage, and was managed successfully.