Craniocervical hypertrophic pachymeningitis.

Surgical neurology international Pub Date : 2025-05-16 eCollection Date: 2025-01-01 DOI:10.25259/SNI_179_2025

Murilo Dos Santos Mancilha, Filipi Fim Andreão, Bárbara de Ávila Costa Januário, Filipe Virgilio Ribeiro, Matheus Nepomuceno Fernandes, Luis Flavio Fabrini Paleare, Bruno Pasqualino Aguilar da Silva, Marcelo Medeiros Felippe, Danilo Gomes Quadros

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Abstract

Background: Hypertrophic pachymeningitis (HP) is a rare neurological disorder characterized by dural thickening. Here, we discuss the diagnosis and surgical management of a 38-year-old whose myelopathy was attributed to dorsally compressive HP extending from the lower cerebellar fossa to C3.

Case description: A 38-year-old male with Sjögren's syndrome presented with cervical pain, upper limb paresis, dysphagia, and left-sided tongue/palate paralysis. The cervical magnetic resonance (MR) showed a dorsally compressive lower cerebellar fossa to C3 lesion. When the biopsy revealed HP, and once conservative treatment failed, the patient successfully underwent a posterior surgical decompression, lesion debulking, and craniocervical fusion.

Conclusion: Cervical HPs should be diagnosed early on MR, and those with significant myelopathy, aggressively surgically treated.

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颅颈肥厚性厚性脑膜炎。

背景：肥厚性厚性脑膜炎（HP）是一种罕见的以硬脑膜增厚为特征的神经系统疾病。在这里，我们讨论了一位38岁的脊髓病患者的诊断和手术治疗，其脊髓病归因于从小脑下窝延伸到C3的背侧压迫性HP。病例描述：一名38岁男性Sjögren综合征患者，表现为颈椎疼痛、上肢麻痹、吞咽困难和左侧舌/腭麻痹。颈磁共振显示背侧压迫下小脑窝至C3病变。当活检显示HP时，一旦保守治疗失败，患者成功地进行了后路手术减压、病变减积和颅颈融合。结论：宫颈hp应在MR中早期诊断，对于有明显脊髓病的患者，应积极进行手术治疗。

本文章由计算机程序翻译，如有差异，请以英文原文为准。

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Surgical neurology international

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