Telescopic pancreatojejunostomy after whipple procedure in FRANTZ Tumor: Case report and literature review

Abstract

Pseudopapillary solid tumour of the pancreas is a rare neoplasm that mainly affects young women and is categorized as a low-grade malignant tumour. Histologically, it does not present specific epithelial differentiation and can originate anywhere in the pancreas; immunohistochemistry is necessary for a definitive diagnosis. This neoplasm usually manifests itself with abdominal pain and a feeling of abdominal mass. Surgery with total resection, Whipple procedure (duodenopancreatectomy), is the treatment of choice, and 5-year survival exceeds 90 % after radical surgery. An end-to-end telescopic pancreatojejunostomy is a safe technique in which the pancreatic remnant is intussuscepted and fully enclosed into the jejunum lumen. It is ideal for a soft pancreas, reducing the risk of pancreatic leakage. We present the case of a 14-year-old female adolescent who presents with abdominal pain, and through imaging, a large pancreatic head tumour was discovered. The patient underwent a Whipple procedure, and the pathological study confirmed a pseudopapillary tumour or Frantz's tumour of the head of the pancreas. The patient had a favourable outcome after the procedure with no complications and tolerated the diet well with no alterations in lifestyle. There was no necessary chemotherapy, and the patient had a strict follow-up with no signs of recurrence.