[Adult Hemorrhagic Moyamoya Disease: Physiopathology and Treatment].

Abstract

The Japan Adult Moyamoya(JAM) Trial revealed the preventive effect of direct bypass on rebleeding in patients with hemorrhagic moyamoya disease. Subsequent studies have elucidated the significance of periventricular anastomosis, a fragile periventricular collateral manifestation, as a source and predictor of hemorrhage. Practitioners should confirm the reduction in periventricular anastomosis after bypass surgery for hemorrhagic moyamoya disease through optimal imaging assessments.