Postrepair Pulmonary Vein Stenosis: Addressing Anatomic and Patient Risk Factors to Improve Outcomes

Abstract

Surgical results for correction of total anomalous pulmonary venous connection (TAPVC) have improved in the current era. Postrepair pulmonary vein stenosis (PR-PVS) remains a major complication following TAPVC repair, often necessitating multiple reinterventions, and impacting patient outcomes. Considerations for patient and anatomical risk factors, surgical techniques for primary TAPVC repair, as well PR-PVS postoperative surveillance and management will be reviewed. We will also touch on emerging areas of research related to PR-PVS pathogenesis and incorporation of patient-specific simulation for surgical planning in TAPVC.