[Diagnosis and treatment of ANCA-associated vasculitis : SHORT VERSION of the S3 guideline of the German Society for Rheumatology and Clinical Immunology e. V. (DGRh) and German Society for Internal Medicine e. V. (DGIM), German Society for Nephrology e. V. (DGfN), German Society for Otorhinolaryngology and Head and Neck Surgery e. V. (DGHNO-KHC), German Ophthalmological Society e. V. (DOG), German Society for Neurology e. V. (DGN), German Society for Pneumology and Respiratory Medicine e. V. (DGP), German Society for Pathology e. V. (DGP), German Radiological Society, Society for Medical Radiology e. V. (DRG), Federal Association of German Pathologists, Federal Kidney Association e. V., German Rheumatism League Federal Association e. V.]

IF 0.9 4区医学 Q4 RHEUMATOLOGY

Zeitschrift fur Rheumatologie Pub Date : 2025-04-01 Epub Date: 2025-04-02 DOI:10.1007/s00393-024-01596-7

J U Holle, T Kubacki, P Aries, B Hellmich, A Kernder, C Kneitz, P Lamprecht, J H Schirmer, A Schreiber, P Berlit, T A Bley, S Blödt, L Decker, K de Groot, S Engel, I Jordans, B Frye, M Haubitz, K Holl-Ulrich, I Kötter, M Laudien, K Milger-Kneidinger, C Muche-Borowski, U Müller-Ladner, T Neß, B Nölle, E Reinhold-Keller, N Ruffer, K Scheuermann, N Venhoff, S von Vietinghoff, T Wiech, M Zänker, F Moosig

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引用次数: 0

Abstract

Vasculitis associated with anti-neutrophil cytoplasmic antibodies (ANCA) is a rare disease with a potentially severe course. Affected patients should be diagnosed as quickly as possible and given suitable treatment according to the current study situation. Considerable progress has been made in the treatment of this disease in recent years, so that a largely evidence-based therapy with immunosuppressants and biologics is now possible. The guideline on the diagnosis and treatment of ANCA-associated vasculitis was raised from S1 level (2017) to S3 level. This guideline is the first German guideline on the diagnosis and treatment of ANCA-associated vasculitis at S3 level.

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[anca相关血管炎的诊断和治疗：德国风湿病和临床免疫学学会S3指南的简短版本e. V.]（DGRh）和德国内科学会e. V。（DGIM），德国肾脏学会e. V.；（DGfN），德国耳鼻咽喉和头颈外科学会e. V。（DGHNO-KHC），德国眼科学会e. V.；（DOG），德国神经学会e. V.；（DGN），德国肺炎和呼吸医学学会e. V。（DGP），德国病理学会e. V.；（DGP），德国放射学会，医学放射学会e. V。（DRG），德国病理学家联邦协会，德国肾脏协会e. V。，德国风湿病联盟联邦协会e. V.]

血管炎伴抗中性粒细胞细胞质抗体（ANCA）是一种罕见的疾病，具有潜在的严重病程。应根据目前的研究情况，尽早诊断并给予适当的治疗。近年来，这种疾病的治疗取得了相当大的进展，因此，现在有可能采用免疫抑制剂和生物制剂进行基于证据的治疗。anca相关性血管炎诊疗指南由2017年S1级提升至S3级。该指南是德国第一个S3水平anca相关血管炎的诊断和治疗指南。

本文章由计算机程序翻译，如有差异，请以英文原文为准。

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来源期刊

Zeitschrift fur Rheumatologie 医学-风湿病学

CiteScore

2.20

自引率

20.00%

发文量

150

审稿时长

6-12 weeks

期刊介绍： Die Zeitschrift für Rheumatologie ist ein international angesehenes Publikationsorgan und dient der Fortbildung von niedergelassenen und in der Klinik tätigen Rheumatologen. Die Zeitschrift widmet sich allen Aspekten der klinischen Rheumatologie, der Therapie rheumatischer Erkrankungen sowie der rheumatologischen Grundlagenforschung. Umfassende Übersichtsarbeiten zu einem aktuellen Schwerpunktthema sind das Kernstück jeder Ausgabe. Im Mittelpunkt steht dabei gesichertes Wissen zu Diagnostik und Therapie mit hoher Relevanz für die tägliche Arbeit – der Leser erhält konkrete Handlungsempfehlungen. Frei eingereichte Originalien ermöglichen die Präsentation wichtiger klinischer Studien und dienen dem wissenschaftlichen Austausch.