G - Hercnan Syndrome (Giant Hand Extraesqueletal Regular Chondroma No Ollier and No Malignant): Report of a Case and Literature Review.

Abstract

Introduction: Extra skeletal chondromas are a subtype of chondroma that constitutes approximately 1.5% of soft tissue tumors; they do not affect the periosteum, cortex, or synovial tissue. They are frequently found in hands and are generally smaller than 3 cm in diameter; few cases are reported larger than 10 cm in diameter.

Case report: A 59-year-old female patient with a history of tumor of 12 cm in diameter in the interdigital region between the first and second of the left hand of 9 years of evolution with involvement of the thumb opposition, with magnetic resonance imaging findings with isointensity in T1 and hyperintensity in T2, without enhancement to gadolinium, She is taken to an excisional biopsy where there is evidence of adherence to the sensory branch of the median nerve, with report of extra skeletal chondroma pathology, with follow-up 1 year post-surgery with total recovery of functionality without evidence of recurrence, additionally tumor with clinical and imaging suggestive of enchondroma in the fifth finger of the left hand and in the frontal region.

Conclusions: We present an unusual clinical case of extra skeletal chondroma of 12 cm in diameter with compromised mobility of the first finger and adherence to the sensory branch of the median nerve, accompanied by suggestive enchondromas in the fifth finger of the same hand and frontal region, without pathological findings of Ollier's disease, malignancy, or recurrence at 1 year of follow-up. We intend to highlight the importance and magnitude, to which extraskeletal chondromas can reach, without being considered benign tumors, they can have important effects due to their mechanical compression.