{"title":"Osteofibrous dysplasia of the 8th rib: a case report.","authors":"Shaivy Malik, Charanjeet Ahluwalia, Sana Ahuja","doi":"10.1007/s12055-024-01785-8","DOIUrl":null,"url":null,"abstract":"<p><p>Osteofibrous dysplasia (OFD) is a rare benign bone lesion primarily affecting the long bones' anterior cortex, commonly observed in adolescents. Typically found in the tibia and fibula, it represents less than 1% of primary bone tumors. While OFD is predominantly seen in the lower extremities, occurrences in ribs, particularly in adult females, are exceptionally rare. Distinguishing OFD from fibrous dysplasia and OFD-like adamantinoma is crucial due to distinct clinical and histopathological features. We illustrate an interesting clinical course of a 28-year-old adult female with monostotic OFD involving the right 8th rib, who was clinically and radiologically suspected to be having fibrous dysplasia (FD). However, histopathological examination assisted in the confirmation of the final diagnosis of OFD. This report presents a case of OFD in the 8th rib of a 28-year-old female, highlighting the diagnostic challenge and emphasizing the importance of accurate diagnosis for appropriate management. The rarity of this presentation underscores the need for further research to elucidate the clinical spectrum and optimal management strategies for OFD in unusual anatomical locations.</p>","PeriodicalId":13285,"journal":{"name":"Indian Journal of Thoracic and Cardiovascular Surgery","volume":"41 3","pages":"314-317"},"PeriodicalIF":0.7000,"publicationDate":"2025-03-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://www.ncbi.nlm.nih.gov/pmc/articles/PMC11832860/pdf/","citationCount":"0","resultStr":null,"platform":"Semanticscholar","paperid":null,"PeriodicalName":"Indian Journal of Thoracic and Cardiovascular Surgery","FirstCategoryId":"1085","ListUrlMain":"https://doi.org/10.1007/s12055-024-01785-8","RegionNum":0,"RegionCategory":null,"ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":null,"EPubDate":"2024/8/2 0:00:00","PubModel":"Epub","JCR":"Q4","JCRName":"CARDIAC & CARDIOVASCULAR SYSTEMS","Score":null,"Total":0}
引用次数: 0
Abstract
Osteofibrous dysplasia (OFD) is a rare benign bone lesion primarily affecting the long bones' anterior cortex, commonly observed in adolescents. Typically found in the tibia and fibula, it represents less than 1% of primary bone tumors. While OFD is predominantly seen in the lower extremities, occurrences in ribs, particularly in adult females, are exceptionally rare. Distinguishing OFD from fibrous dysplasia and OFD-like adamantinoma is crucial due to distinct clinical and histopathological features. We illustrate an interesting clinical course of a 28-year-old adult female with monostotic OFD involving the right 8th rib, who was clinically and radiologically suspected to be having fibrous dysplasia (FD). However, histopathological examination assisted in the confirmation of the final diagnosis of OFD. This report presents a case of OFD in the 8th rib of a 28-year-old female, highlighting the diagnostic challenge and emphasizing the importance of accurate diagnosis for appropriate management. The rarity of this presentation underscores the need for further research to elucidate the clinical spectrum and optimal management strategies for OFD in unusual anatomical locations.
期刊介绍:
The primary aim of the Indian Journal of Thoracic and Cardiovascular Surgery is education. The journal aims to dissipate current clinical practices and developments in the area of cardiovascular and thoracic surgery. This includes information on cardiovascular epidemiology, aetiopathogenesis, clinical manifestation etc. The journal accepts manuscripts from cardiovascular anaesthesia, cardiothoracic and vascular nursing and technology development and new/innovative products.The journal is the official publication of the Indian Association of Cardiovascular and Thoracic Surgeons which has a membership of over 1000 at present.DescriptionThe journal is the official organ of the Indian Association of Cardiovascular-Thoracic Surgeons. It was started in 1982 by Dr. Solomon Victor and ws being published twice a year up to 1996. From 2000 the editorial office moved to Delhi. From 2001 the journal was extended to quarterly and subsequently four issues annually have been printed out at time and regularly without fail. The journal receives manuscripts from members and non-members and cardiovascular surgeons. The manuscripts are peer reviewed by at least two or sometimes three or four reviewers who are on the panel. The manuscript process is now completely online. Funding the journal comes partially from the organization and from revenue generated by subscription and advertisement.