Reichel Syndrome in Children: A Case Report.

Q3 Medicine
Revista Brasileira de Ortopedia Pub Date : 2024-12-27 eCollection Date: 2024-11-01 DOI:10.1055/s-0044-1779511
Hanene Lassoued Ferjani, Hiba Bettaib, Ben Nessib Dorra, Kaouther Maatallah, Mourad Jenzri, Wafa Hamdi
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引用次数: 0

Abstract

Reichel syndrome or primary synovial chondromatosis (PSC) is an uncommon benign metaplastic condition that usually affects large joints. Though shoulder involvement was scarce, there are only a few cases in the pediatric population. A 14- year-old boy was admitted to the Pediatric Orthopedics department with right shoulder pain for 14 months. Imaging revealed multiple loose bodies distributed throughout the glenohumeral joint. Upon the arthroscopic approach, we remove all cartilaginous nodules within the glenohumeral space and abarticular tendon. Histopathologic examination confirmed the diagnosis of primary synovial chondromatosis. At follow-up, the patient remains free of symptoms, and shoulder radiographs showed no recurrence of calcification. The present case illustrates the clinical patterns, imaging features, histological findings, and therapeutic management of shoulder primary synovial chondromatosis in a pediatric patient.

儿童Reichel综合征1例报告。
Reichel综合征或原发性滑膜软骨瘤病(PSC)是一种罕见的良性化生疾病,通常影响大关节。虽然肩部受累的病例很少,但在儿科人群中只有少数病例。一名14岁男孩因右肩疼痛14个月入院儿科骨科。影像学显示多个松散体分布于整个盂肱关节。经关节镜入路,我们切除肱骨盂间隙和关节外肌腱内的所有软骨结节。组织病理学检查证实为原发性滑膜软骨瘤病。随访时,患者无症状,肩部x线片显示没有钙化复发。本病例阐述了一名儿童肩关节原发性滑膜软骨瘤病的临床模式、影像学特征、组织学表现和治疗管理。
本文章由计算机程序翻译,如有差异,请以英文原文为准。
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来源期刊
CiteScore
1.00
自引率
0.00%
发文量
142
审稿时长
21 weeks
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