Extra pulmonary pleuropulmonary blastoma in two-year-old child: a rare cystic lesion of lung

Abstract

Pleuropulmonary blastoma (PPB) is a rare but fatal intrathoracic malignancy, which arises from the lung parenchyma and/or pleura. Despite being rare, PPB is the most common lung tumor in young children. Clinically, this rare malignancy is often mistaken for symptoms of respiratory tract infection or pneumothorax. The PPB require aggressive treatment which include surgical resection and chemotherapy. We report this case with the aim to raise awareness about this fatal and misleading malignancy. Knowledge of clinical presentation, imaging findings, histopathological findings, staging and association with other tumors is crucial for timely diagnosis of pleuropulmonary blastoma and subsequent adequate management.