Miguel A. Medina-Andrade , Ítalo D. Masini-Aguilera , Jaime Lopez-Taylor , David Ramírez-Cedillo , Carlos A. Jimenez-Fernandez , Nancy Erika Medina Martinez , Rocio A. Peña-Juárez
{"title":"Reparación de ectopia cordis asociada con pentalogía de Cantrell, presentación de un caso","authors":"Miguel A. Medina-Andrade , Ítalo D. Masini-Aguilera , Jaime Lopez-Taylor , David Ramírez-Cedillo , Carlos A. Jimenez-Fernandez , Nancy Erika Medina Martinez , Rocio A. Peña-Juárez","doi":"10.1016/j.circv.2024.04.002","DOIUrl":null,"url":null,"abstract":"<div><div>Cantrelĺs pentalogy is an extremely rare syndrome associating with ectopia cordis and various degrees of midline defects. We present the case of patient with pentalogy of Cantrell with ectopia complete cordis without serious intracardiac anomalies, performing cardiac reduction towards the mediastinum with adequate evolution.</div></div>","PeriodicalId":42671,"journal":{"name":"Cirugia Cardiovascular","volume":"32 1","pages":"Pages 23-25"},"PeriodicalIF":0.3000,"publicationDate":"2025-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":"0","resultStr":null,"platform":"Semanticscholar","paperid":null,"PeriodicalName":"Cirugia Cardiovascular","FirstCategoryId":"1085","ListUrlMain":"https://www.sciencedirect.com/science/article/pii/S1134009624000810","RegionNum":0,"RegionCategory":null,"ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":null,"EPubDate":"","PubModel":"","JCR":"Q4","JCRName":"SURGERY","Score":null,"Total":0}
引用次数: 0
Abstract
Cantrelĺs pentalogy is an extremely rare syndrome associating with ectopia cordis and various degrees of midline defects. We present the case of patient with pentalogy of Cantrell with ectopia complete cordis without serious intracardiac anomalies, performing cardiac reduction towards the mediastinum with adequate evolution.