Novel Peri-Operative Strategy for Sickle Cell Disease with Tetralogy of Fallot.

IF 1.1 Q3 ANESTHESIOLOGY

Annals of Cardiac Anaesthesia Pub Date : 2024-07-01 Epub Date: 2024-07-04 DOI:10.4103/aca.aca_215_23

Naveed Khan, Vaibhav Dhabe, Ameya Kaskar, Parthiban Kuppusamy, Supratim Sen, Gaurav Kumar

引用次数: 0

Abstract

Abstract: Peri-operative management of cyanotic congenital heart disease in a patient of sickle cell disease (SCD) can be challenging. We report a case of Tetralogy of Fallot and homozygous SCD with history of multiple blood transfusions and sickle cell crises who underwent intracardiac repair. Hemoglobin S level was reduced from 75% pre-operative to 21.8% postoperative with a combination of pre-operative blood transfusion, intraoperative exchange transfusion, and normothermic cardiopulmonary bypass (CPB). Pre-operative optimization and safe intraoperative conduct were essential to avoid sickling crises.

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镰状细胞病合并法洛氏四联症手术前的新策略

摘要：镰状细胞病（SCD）患者紫绀型先天性心脏病的围手术期管理可能具有挑战性。我们报告了一例法洛四联症和同型 SCD 病例，患者有多次输血史和镰状细胞危象，并接受了心内修复术。通过术前输血、术中换血和常温心肺旁路（CPB），血红蛋白 S 水平从术前的 75% 降至术后的 21.8%。术前优化和术中安全操作对避免镰状细胞危机至关重要。

本文章由计算机程序翻译，如有差异，请以英文原文为准。

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来源期刊

Annals of Cardiac Anaesthesia ANESTHESIOLOGY-

CiteScore

1.60

自引率

0.00%

发文量

147

审稿时长

26 weeks

期刊介绍： Annals of Cardiac Anaesthesia (ACA) is the official journal of the Indian Association of Cardiovascular Thoracic Anaesthesiologists. The journal is indexed with PubMed/MEDLINE, Excerpta Medica/EMBASE, IndMed and MedInd. The journal’s full text is online at www.annals.in. With the aim of faster and better dissemination of knowledge, we will be publishing articles ‘Ahead of Print’ immediately on acceptance. In addition, the journal would allow free access (Open Access) to its contents, which is likely to attract more readers and citations to articles published in ACA. Authors do not have to pay for submission, processing or publication of articles in ACA.