Saddled by the Saddle Nose: A Case of Wegener's Granulomatosis

K. Shilpa, Heera Ramesh, S. Somashekhar, B. Leelavathy
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引用次数: 0

Abstract

Wegener's Granulomatosis with polyangiitis (GPA) is a systemic disease of unknown etiology characterized by necrotizing granulomatous inflammation, tissue necrosis, and variable degrees of vasculitis in small- and medium-sized blood vessels. The classical clinical triad consists of involvement of the upper airways, lungs, and kidneys. Saddle-nose deformity is a well-recognized complication of GPA but more commonly occurs due to leprosy, trauma, cocaine abuse, and sarcoidosis. Since this entity is not commonly encountered in our country, we present a unique case of a middle-aged woman presenting with saddle-nose deformity and the diagnostic dilemmas faced by us. This case is being reported due to its rarity in Indian literature.
鞍鼻:韦格纳肉芽肿病的一个病例
韦格纳肉芽肿伴多血管炎(GPA)是一种病因不明的全身性疾病,以坏死性肉芽肿炎症、组织坏死和不同程度的中小血管炎为特征。典型的临床三联征包括上呼吸道、肺部和肾脏受累。鞍鼻畸形是一种公认的 GPA 并发症,但更常见于麻风病、创伤、可卡因滥用和肉样瘤病。由于这种病症在我国并不常见,我们在此介绍一例独特的中年女性鞍鼻畸形病例,以及我们所面临的诊断难题。由于该病例在印度文献中十分罕见,我们特此报告。
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