Dyke-Davidoff-Masson Syndrome: A Rare Presentation

Abstract

Dyke-Davidoff-Masson syndrome (DDMS) is characterized by seizures, facial asymmetry, contralateralhemiplegia and mental retardation. The characteristic radiological features are cerebral hemiatrophy with homolateralhypertrophy of skull and sinuses. Case report: We report a case of DDMS in a 41-year-old female who presented withgeneralized tonic-clonic seizures, hemiparesis of the right upper and lower limb with deviation of the mouth to left.Noncontrast computed tomography (NCCT) head and magnetic resonance imaging (MRI) revealed hemiatrophy of the rightcerebral hemisphere. Conclusion: DDMS is a rare disease; hence, diagnosing and managing such patients may be challenging.Our aim is to draw attention of the treating physicians towards this disease with the help of this case report.