Complex Adult Congenital Heart Disease: A Rare Case of Dextrocardia with Double-outlet Right Ventricle

Adeola Olubunmi Ajibare, Oluwaseye Michael Oladimeji, Oluwafemi Tunde Ojo, Folasade Adeola Daniel, Philip Alaba Adebola, Abdulazeez Olanrewaju
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引用次数: 0

Abstract

Abstract Double-outlet right ventricle (DORV) is a complex and rare congenital heart disease (CHD), which is usually symptomatic early in childhood and thus diagnosed early. Dextrocardia is another rare CHD that can occur either as an isolated cardiac abnormality or may be associated with other complex cardiac defects. However, the co-occurrence of DORV and dextrocardia is rare, especially in adult life. We present a 35-year-old Nigerian lady with situs inversus totalis and complex CHD, which included dextrocardia with multiple congenital intracardiac shunts, DORV occurring with L-malpositioning of the great vessels, atrial septal defect, and ventricular septal defect with partial anomalous pulmonary venous drainage, persistent left superior vena cava as well as severe pulmonary stenosis.
复杂成人先天性心脏病:右心双出口右心室一例
摘要双出口右心室(DORV)是一种复杂而罕见的先天性心脏病(CHD),通常在儿童早期出现症状,因此诊断较早。右心是另一种罕见的冠心病,既可以作为孤立的心脏异常发生,也可能与其他复杂的心脏缺陷相关。然而,DORV和右心同时出现是罕见的,尤其是在成人生活中。我们报告一名35岁的尼日利亚女性,患有完全性倒位和复杂的冠心病,包括右心伴多重先天性心内分流,DORV伴大血管l位错位,房间隔缺损,室间隔缺损伴部分肺静脉异常引流,持续性左上腔静脉以及严重的肺狭窄。
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来源期刊
自引率
0.00%
发文量
65
审稿时长
20 weeks
期刊介绍: The Nigerian Journal of Medicine publishes articles on socio-economic, political and legal matters related to medical practice; conference and workshop reports and medical news.
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