Pseudosarcomatous Myofibroblastic Proliferation, A Rare Bladder Condition Successfully Managed with Partial Cystectomy - A Case Report and Literature Review

Abstract

Purpose: Pseudosarcomatous fibromyxoid tumors of the genitourinary tract are rare tumors that can be a surgical emergency, presenting with relentless gross hematuria. While the majority of cases reported in the literature describe transurethral resection as the initial approach, poor visibility and large tumor burden, particularly in the pediatric population, may obviate successful management. We reviewed the literature and report a case in which the bleeding mass was acutely managed with an open partial cystectomy with no long-term complications, including no tumor recurrence or progression. Case Presentation: A healthy 16 year-old, non-smoking male presented with severe gross hematuria causing hemodynamically instability requiring management with open partial cystectomy. Initial transurethral resection was attempted, however poor visibility and large tumor burden prevented adequate resection. The case was converted to an open approach and a partial