Amyloidosis in ENT Presentation of a Case

Abstract

Amyloidoses are a heterogeneous group of rare diseases that consist of the abnormal folding of a precursor protein that ends up being deposited in the form of fibrillar structures in various organs and systems. It can present as a hereditary or isolated disease, localized or systemic, primary (idiopathic) or secondary to infectious processes such as tuberculosis, leprosy and osteomyelitis or chronic inflammatory processes such as rheumatoid arthritis. Within the clinical manifestations, vague symptoms and signs appear, depending on the location and size of the deposits, since the heart, kidneys, liver, gastrointestinal tract, peripheral nervous system, lungs, soft tissues, etc. may be affected. Therefore, it is of utmost importance that once the diagnosis is confirmed, a systemic study is performed to evaluate the extensión of the disease to other possible target organs. We present the case of a 59-year-old man, with a lesion in the upper pole of the right tonsil, positive for amyloidosis. Objective: Present the case of amyloidosis in an extremely rare location, for the dissemination and knowledge of the disease.