Childhood Onset Erythrokeratoderma En Cocardes Treated with Oral Acitretin

Abstract

Erythrokeratodermas are genodermatoses of keratinisation which usually presents in infancy. Erythrokeratoderma en cocardes is a rare variant of erythrokeratoderma which present as polycyclic hyperkeratotic plaques with a peripheral desquamation, forming a concentric appearance termed ‘en cocarde’. Here, we report a case of erythrokeratoderma en cocardes with onset in childhood showing excellent response after 2 months of acitretin therapy.