Fibrodysplasia Ossificans Progressiva: TMJ Involvement and Feeding Dilemma

Abstract

Fibrodysplasia ossificans progressiva (FOP) is catastrophic uncommon hereditary connective tissue disease. The disease clinically presented as progressive ossification of ligaments, tendons as well as facial and skeletal muscles starting early in life. First presentation is painful localized soft tissue swellings. Articular dysfunction and limitation of movements is significant with involvement of the spine and proximal extremities. Limitation of mouth opening secondary to Tempromandibular joint (TMJ) involvement is late presentation of the disease. Unfortunately, surgical intervention of such condition is mentioned in literature with a very poor outcome. In this manuscript we report a case of FOP presented with limited mouth opening three months after dental extraction. Clinical findings, radiographs, and proposed treatment option are discussed.