A rare and challenging mitral valve replacement in a child with Hurler syndrome

Abstract

Mucopolysaccharidoses are progressive inherited lysosomal storage disorders, and early cardiac involvement is common. Valvular involvement of mucopolysaccharidoses usually causes regurgitation, most commonly affecting the left heart and mitral valve. In this case, we discuss the treatment and perioperative management of mitral valve degeneration in a child with Hurler syndrome by performing mitral valve replacement.