Malignant intracerebral nerve sheath tumour of the brain presenting as a recurrent meningioma

Abstract

A malignant intracerebral nerve sheath tumour (MINST) is a variant of MPNST arising inside the brain. They are very rare tumours that are aggressive and have strong metastatic potential. We report a case of a recurrent lesion in the brain in a 39 years male who presented as recurrent meningioma. It was finally reported as MINST with histopathology and immunohistochemistry. Surgical excision is the treatment of choice. The patient is on follow-up after an uneventful surgical excision. To the best of our knowledge, very few cases of malignant intracerebral nerve sheath tumours have been reported so far in the literature. This case is presented not only for its rarity but also to highlight that this aggressive tumour needs to be kept in mind while diagnosing such lesions with these histomorphological findings.