Rapid Improvement of Scleromyxedema Associated With IgG Kappa Monoclonal Gammopathy After Intravenous Immunoglobulin (IVIG)

Dillon D. Clarey, M. Arthur, E. Blue, E. Mata, C. Georgesen
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Abstract

interstitial between collagen bundles. for scleromyxedema, and protein electrophoresis demonstrated IgG kappa monoclonal gammopathy. Subsequent bone marrow biopsy a kappa plasma change for Raynaud’s a with a speckled pattern, anti-Scl-70, and anti-centromere antibodies. for of IgG kappa, rather than monoclonal
静脉注射免疫球蛋白(IVIG)后IgG κ单克隆γ病相关硬黏液水肿的快速改善
胶原束之间的间隙。蛋白电泳显示IgG kappa单克隆γ病。随后的骨髓活组织检查显示雷诺氏a型kappa血浆改变伴斑点型,抗scl -70和抗着丝粒抗体。而非单克隆
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