A Rarely Seen Case: Congenital Cystic Adenomatoid Malformation, Type 0

Abstract

Konjenital kistik adenomatoid malformasyon (KKAM), tüm doğumsal akciğer anomalilerin 1/4’ünü teşkil eden hamartomatöz bir akciğer anomalisidir. Beş subtipe ayrılır. Sunulan olgu ile çok nadir görülen Tip 0’ın literatürdeki olgu Type 0 in the literature which is very rare type. A term baby girl at 40 th weeks of gestation, from a 19-year-old mother was delivered. The APGAR score of baby was determined 1-1 and baby was intubated. Detection of left sided pneumothorax a chest tube placed. But the baby could not survive after resuscitation period. After the histopathological examination of the lungs it was diagnosed as CCAM Type 0 (bilateral diffuse). By the presented case, this pathology is described with all its detectable aspects, the anomalies that may accompany, how the histopathological samples should be taken. It is intended to be shared with forensic medicine specialists, pathologists and pediatrics specialists.