Alveolar soft part sarcoma of the mandible: A rare case

Abstract

Alveolar soft part sarcoma (ASPS) is an enigma both for clinicians and pathologists. It is a rare soft tissue neoplasm affecting young adults. A 72-year-old female presented with a history of painful ulcer on the right side of the oral cavity associated with bleeding and difficulty in chewing. She underwent wide local excision of the lesion with segmental mandibulectomy and supraomohyoid neck dissection. Histopathological examination was suggestive of ASPS with involvement of resection margins. The patient developed rapid relapse after surgery and did not respond to chemotherapy and radiotherapy. She ultimately died of disease 10 months postsurgery.