Scimitar Syndrome: Infra-Diaphragmatic Form a Novel Surgical Approach

Abstract

Scimitar syndrome is a complex malformation in which the main feature is a partial anomalous venous drainage of the right side toward the inferior vena cava or the portal system. There are anomalies associated in bronchopulmonary segmentation and vascular lung connections [1]. In 1836 in specimens of autopsy Cooper in London published the first description and later Chassinat in París [2, 3]. In 1949 Dotter et, al through angiocardiography shown the first clinical diagnosis where noted the particular appearance of the anomalous vein on x-ray of thorax [4]. Later Neill et, al in 1960 called the scimitar sign for describing this anomaly [5]. Drake and Lynch in 1950 performed the first surgical management of this disease [6]. Later the first physiological correction of anomalous venous drainage was published in 1956 by Kirklin et, al [7]. Finally Neill CA, et al. published the familial occurrence of Scimitar syndrome.