Hemophilia C in maxillofacial surgery – A rare finding

Abstract

Factor XI (FXI) deficiency or hemophilia C is a very rare, autosomal recessive bleeding disorder. Patients with this deficiency do not typically show spontaneous bleeding or any specific symptoms. Those who have this disorder are seldom identified during situations such as trauma or surgery or during pre-surgical workups. Hence, operating on such patients, especially those with intraoral or vascular tumors, is particularly associated with a high bleeding risk. Therefore, great care must be taken when treating patients with disorders such as FXI deficiency. There are very few reports that address the management of patients with bleeding disorders in maxillofacial vascular lesions. Here, we report a patient with FXI deficiency, who underwent surgical excision of pyogenic granuloma of her upper right alveolus under general anesthesia and describe all the measures taken to reduce the chances of excessive bleeding.