[Autonomic nervous system disorders in 230 cases of basilar impression and Arnold-Chiari deformity].

Neurochirurgia Pub Date : 1992-11-01
J A da Silva, J C Brito, P V da Nóbrega
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Abstract

Within the period of 1971 to 1989 we operated on 230 cases of craniocervical malformations characterised by 189 cases of basilar impression associated with Arnold-chiari malformation, 28 cases of isolated basilar impression and 13 cases of Arnold-Chiari malformation. Autonomic disturbance was observed in 136 (59.1%) cases: sexual disorders like reduced potency and impotency were observed in 86 (60.9%) out of 141 male patients, urinary symptoms in 39 (17%) patients; and other autonomic features like dyspnea, anhidrosis, hyperhidrosis, Claude Bernard-Horner syndrome and constipation in 41 (17.8%) patients.

【230例基底压痕及Arnold-Chiari畸形自主神经系统障碍分析】。
在1971年至1989年期间,我们对230例颅颈畸形进行了手术治疗,其中颅底压痕合并Arnold-chiari畸形189例,孤立颅底压痕28例,Arnold-chiari畸形13例。136例(59.1%)患者出现自主神经障碍;141例男性患者中出现性能力下降、阳痿等性功能障碍86例(60.9%),泌尿系统症状39例(17%);41例(17.8%)患者出现呼吸困难、无汗、多汗症、Claude Bernard-Horner综合征和便秘等自主神经特征。
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