Fahr’s Disease with a Thirty Years History of Seizures.

Abstract

Fahr's disease/Fahr's syndrome is a rare neurological disorder characterized by symmetrical calcification in various brain parts, most commonly in the basal ganglia. We report a case of Fahr's disease in a 72 -years-old female who presented with delirium. Upon further evaluation, she had a history of seizures for thirty years, dementia for eighteen months, extrapyramidal symptoms for one year and psychiatric symptoms for six months. We diagnosed this case as Fahr's disease and managed in the intensive care unit and wards. We discharged her with medications like tetrabenazine, quetiapine, clonazepam, atorvastatin, donepezil, sodium valproate, vitamins and mineral supplements. We followed her progress for seven months. Her motor and neuro-psychiatric recovery during the period has been encouraging. This report highlights the importance of screening for Fahr’s disease in any case of seizure and bilateral brain calcification, which is highly overlooked and misdiagnosed in our part of the world.