A Case of Incontinentia Pigmenti in a New Born

Abstract

Incontinentia pigmenti (IP) is a rare neuroectodermal dysplasia with an estimated incidence of 0.7 cases per 100,000 births. Up to date approximately 1,200 cases have been reported in scientific literature. IP has a multisystemic involvement where the skin manifestations are the hall mark and could be seen even at birth. We present a baby girl with typical skin manifestations of IP seen at birth.