EMBRYONAL RHABDOMYOSARCOMA OF THE COMMON BILE DUCT: A CASE REPORT AND REVIEW OF THE LITERATURE

Abstract

Embryonal rhabdomyosarcoma (ERMS) of the biliary tree is a rare tumor that commonly arises from the common bile duct. The most common clinical features are obstructive jaundice and abdominal pain. Diagnostic imaging techniques including ultrasound (US), computerized tomography (CT) scan, and magnetic resonance cholangiopancreatography (MRCP) are useful in the diagnosis and evaluation of biliary tree anatomy. Once believed to be an incurable disease, the outcome for patients with biliary RMS has improved with a multidisciplinary treatment approach, including appropriate surgery, chemotherapy, and radiation. Herein we describe a case of three years old child with Embryonal rhabdomyosarcoma originating in the common bile duct who was treated with surgery, chemotherapy according to European Soft tissue Sarcoma Group (EpSSG) protocol and adjuvant postoperative Intensity Modulated Radiotherapy (IMRT) to surgical bed with 6 MV photons to a dose of 41,4Gy in 23 fractions.