{"title":"Complex Tuberous Sclerosis Associated with Pulmonary Lymphangioleiomyomatosis","authors":"Dal Maso Vinicius","doi":"10.24966/PMRR-0177/100020","DOIUrl":null,"url":null,"abstract":"Complex Tuberous Sclerosis Associated with Pulmonary Lymphangioleiomyomatosis. J Pulm Med Respir Res 5: 020. Abstract Complex tuberous sclerosis is an autosomal dominant, sporadic, or familial neurocutaneous disease that affects multiple organs and systems, commonly leads to lymphangioleiomyomatosis and benign tumors in various tissues, possibly evolving with organic dysfunction. We present a case of complex tuberous sclerosis associated with lymphangioleiomyomatosis, whose initial presentation was bilateral pneumothorax,","PeriodicalId":281819,"journal":{"name":"Pulmonary Medicine & Respiratory Research","volume":"74 1","pages":"0"},"PeriodicalIF":0.0000,"publicationDate":"2019-01-30","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":"1","resultStr":null,"platform":"Semanticscholar","paperid":null,"PeriodicalName":"Pulmonary Medicine & Respiratory Research","FirstCategoryId":"1085","ListUrlMain":"https://doi.org/10.24966/PMRR-0177/100020","RegionNum":0,"RegionCategory":null,"ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":null,"EPubDate":"","PubModel":"","JCR":"","JCRName":"","Score":null,"Total":0}
引用次数: 1
Abstract
Complex Tuberous Sclerosis Associated with Pulmonary Lymphangioleiomyomatosis. J Pulm Med Respir Res 5: 020. Abstract Complex tuberous sclerosis is an autosomal dominant, sporadic, or familial neurocutaneous disease that affects multiple organs and systems, commonly leads to lymphangioleiomyomatosis and benign tumors in various tissues, possibly evolving with organic dysfunction. We present a case of complex tuberous sclerosis associated with lymphangioleiomyomatosis, whose initial presentation was bilateral pneumothorax,