Kasabach-Merritt Syndrome In A Patient With Klippel-Trenaunay Syndrome Undergoing Massive Transfusion.

Abstract

We present the case of a patient with extensive Klippel-Trenaunay Syndrome and underlying Kasabach Merritt Syndrome who encountered extensive intraoperative bleeding requiring a massive transfusion of greater than thirty liters of blood and blood products. This case highlights the coagulation challenges posed not only by massive transfusion but also by Klippel-Trenaunay Syndrome with concomitant Kasabach-Merritt Syndrome. This case also notes the value of massive transfusion protocols, while keeping in mind that these have been created from retrospective data.