Arrhythmogenic Right Ventricular Cardiomyopathy - A Case Report

Abstract

Arrhythmogenic right ventricular cardiomyopathy (ARVC), formerly called "arrhythmogenic right ventricular dysplasia/cardiomyopathy" (ARVD/ARVC), is a myocardial structural abnormality disease with clinical presentation of cardiac arrhythmia. It is characterized by the replacement of the myocardium with fibrofatty tissue. In 2010, Marcus et al. proposed revised criteria based on the original Task Force Criteria 1994. We present a case of a young African American male who met two major criteria for definite diagnosis of ARVC: Electrocardiogram (EKG) major criteria and Magnetic Resonance Imaging (MRI) major criteria. The patient had early transition inverted t waves in lead V1-V4, and MRI showed Right Ventricle (RV) dyskinesia with RV Ejection Fraction (EF) < 40%, both satisfying the two major criteria required for definitive diagnosis of ARVC.