Congenital Esophageal Stenosis in Children: From Etiology to Prognosis

Soo-Hong Kim, Hyun Young Kim
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引用次数: 1

Abstract

Congenital esophageal stenosis (CES) is a rare disease that has been reported to occur once in every 25,000 to 50,000 births. According to its etiology, CES is divided into 3 subtypes, tracheobronchial remnants (TBR), fibromuscular hypertrophy (FMH) and membranous diaphragm (MD). Symptoms begin at the weaning period and the introduction of solid food around 6 months with dysphagia and vomiting. Esophagography is first screening test and endoscopic ultrasonography plays important roles to diagnose subtypes deciding therapeutic plan. TBRs were generally treated with surgical resection and end-to-end anasotomosis, whereas FMH and MD had good response rate to endoscopic or radiologic guided dilatation. This article reviews the literature on the etiology, clinical course, diagnosis and management of CES including recent opinion.
儿童先天性食管狭窄:从病因到预后
先天性食管狭窄(CES)是一种罕见的疾病,据报道每25,000至50,000个新生儿中就会发生一次。根据其病因,可分为气管支气管残余(TBR)、纤维肌肥大(FMH)和膜性膈肌(MD) 3种亚型。症状开始于断奶期,6个月左右开始进食固体食物,伴有吞咽困难和呕吐。食管造影是第一筛检,超声内镜检查对诊断亚型决定治疗方案具有重要作用。tbr一般采用手术切除和端到端吻合治疗,而FMH和MD对内镜或放射学引导下的扩张有良好的反应率。本文综述了有关该病的病因、临床过程、诊断和治疗的文献,包括最近的观点。
本文章由计算机程序翻译,如有差异,请以英文原文为准。
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