Superior Segmental Optic Nerve Hypoplasia Presenting With Exotropia and Nystagmus – Case Report

Abstract

Superior segmental optic nerve hypoplasia (SSONH) is a developmental disorder of the disc with unclear pathogenesis causing inferior altitudinal field loss. Dissociated vertical deviation (DVD) usually occurs with unequal visual input owing to early strabismus like infantile esotropia. Occurrence of DVD in a case of SSONH as a presenting complaint has never been reported earlier. We report a case of a young boy with SSONH presenting with exotropia and DVD. Our case shows the occurrence of dissociated strabismus like DVD in child with inferior altitudinal field loss owing to SSONH which is noted as a rare association