Retiform hemangioendothelioma: A rare case of slow growing vascular tumor with review of literature

Abstract

Retiform hemangioendotheliomas are extremely rare tumors of vascular origin. Overall incidence of hemangioendothelioma being <1/1000000. They are low grade angiosarcomas with little risk of metastasis. It usually occurs as a single skin or subcutaneous lesion on the trunk or extremities commonly seen in middle aged adults [1] . Due to its rarity no well-defined guidelines are there for its management, follow up and dealing with local recurrence [2] . Therefore we would like to discuss the case of Retiform Hemangioendothelioma over scapular region in an adult lady which presented with its classical features and how it was managed.