{"title":"Paper box fixation for femur fractures in an infant with osteogenesis imperfecta","authors":"Takeshi Sato, Satsuki Nakano, Arihiko Kanaji, Tomohiro Ishii, Tomonobu Hasegawa","doi":"10.1111/cga.12495","DOIUrl":null,"url":null,"abstract":"Osteogenesis imperfecta (OI) is a congenital disorder characterized by fragile bones. Infants with OI often develop fractures during daily care even when caution is exercised. When splints or casts are used to treat fractures in infants with OI, additional splint- or cast-associated fractures may occur owing to the bone fragility. 1 To date, safe methods of fixation without the use of splints or casts have not been established. 2,3 Here, we present our method of fixing femur fractures in an infant with OI using a paper box. Our patient was detected with short lower limbs at approximately 18 gestational weeks by routine ultrasonography. She was born at 37 gestational weeks by elective cesarean section. She was diagnosed with OI type IV based on radiological findings, which included retarded ossification of the cranial vault, generalized demineralization, slender long bones, and bowing of long bones with microfractures. Pamidronate","PeriodicalId":10626,"journal":{"name":"Congenital Anomalies","volume":null,"pages":null},"PeriodicalIF":1.3000,"publicationDate":"2022-09-18","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":"0","resultStr":null,"platform":"Semanticscholar","paperid":null,"PeriodicalName":"Congenital Anomalies","FirstCategoryId":"3","ListUrlMain":"https://onlinelibrary.wiley.com/doi/10.1111/cga.12495","RegionNum":4,"RegionCategory":"医学","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":null,"EPubDate":"","PubModel":"","JCR":"Q3","JCRName":"PEDIATRICS","Score":null,"Total":0}
引用次数: 0
Abstract
Osteogenesis imperfecta (OI) is a congenital disorder characterized by fragile bones. Infants with OI often develop fractures during daily care even when caution is exercised. When splints or casts are used to treat fractures in infants with OI, additional splint- or cast-associated fractures may occur owing to the bone fragility. 1 To date, safe methods of fixation without the use of splints or casts have not been established. 2,3 Here, we present our method of fixing femur fractures in an infant with OI using a paper box. Our patient was detected with short lower limbs at approximately 18 gestational weeks by routine ultrasonography. She was born at 37 gestational weeks by elective cesarean section. She was diagnosed with OI type IV based on radiological findings, which included retarded ossification of the cranial vault, generalized demineralization, slender long bones, and bowing of long bones with microfractures. Pamidronate
期刊介绍:
Congenital Anomalies is the official English language journal of the Japanese Teratology Society, and publishes original articles in laboratory as well as clinical research in all areas of abnormal development and related fields, from all over the world. Although contributions by members of the teratology societies affiliated with The International Federation of Teratology Societies are given priority, contributions from non-members are welcomed.