天疱疮评分系统及其有效性研究-文献综述

IF 2.3 4区医学 Q2 DERMATOLOGY

Dermatologica Sinica Pub Date : 2023-04-01 DOI:10.4103/ds.DS-D-22-00150

Darby Boucher, Anna L. Wilson, Dedee Murrell

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引用次数: 1

摘要

天疱疮是一种罕见的自身免疫性起泡疾病，影响皮肤和粘膜。尽管最近在治疗方面取得了进展，但天疱疮与高患者死亡率有关，并对患者的生活质量和心理健康产生了显著的负面影响。有效的评分系统，以准确测量天疱疮的严重程度是至关重要的疾病活动监测，治疗效果评估和试验，比较和引进新的治疗方法。本文回顾了现有的天疱疮评分系统及其验证研究，并提出了一个未来的研究领域，关于天疱疮严重程度的简单评分的全球评估。

本文章由计算机程序翻译，如有差异，请以英文原文为准。

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Pemphigus scoring systems and their validation studies – A review of the literature

Pemphigus is a rare autoimmune blistering disease that affects the skin and mucous membranes. Despite recent advances in treatment, pemphigus is associated with high patient mortality and has a significantly negative impact on patients' quality of life and mental health. Validated scoring systems to accurately measure pemphigus severity are vital for the monitoring of disease activity, evaluation of treatment efficacy and trialing, comparison and introduction of new treatments. This article reviews the existing scoring systems for pemphigus and their validation studies and proposes a future area of research regarding global assessments for simplistic scoring of pemphigus severity.

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来源期刊

Dermatologica Sinica DERMATOLOGY-

CiteScore

2.80

自引率

20.00%

发文量

审稿时长

>12 weeks

期刊介绍： Dermatologica Sinica aims to publish high quality scientific research in the field of dermatology, with the goal of promoting and disseminating dermatological-related medical science knowledge to improve global health. Articles on clinical, laboratory, educational, and social research in dermatology and other related fields that are of interest to the medical profession are eligible for consideration. Review articles, original articles, brief reports, case reports and correspondence are accepted.