Persistent left superior vena cava with absent right superior vena cava in a patient with a secundum atrial septal defect

We present a case report of an 11 year old patient, with SitusSolitus, normal segmental anatomy, persistent Left Superior Vena Cava (LSVC) draining into the coronary sinus and absent Right Superior Vena Cava (RSVC). The peculiarity of this presentation was the combination of a LSVC with a secundum Type Atrial Septal Defect (ASD), instead of the more common association to sinus venosus type ASD. From this case, we learned that surgical team’s professional experience on rare cardiological pathogenic conditions is the key for survival of patients.