{"title":"梅干腹综合征合并先天性膀胱-脐下皮肤瘘1例","authors":"A. Abuhamda, E. Mazen","doi":"10.21767/2386-5180.100254","DOIUrl":null,"url":null,"abstract":"Prune Belly Syndromes (PBS) usually fatal unless there is a communication between the fetal bladder and the amniotic sac. We report a case of PBS with congenital vesico-subumbilical skin fistula in a Palestinian male neonate. The patient had defect abdominal muscles, wrinkled abdominal skin, cryptorchidism, urethral atresia, vesico-subumbilical skin fistula and normal kidney function. Baby was discharged home in general condition with once daily prophylactic dose of oral amoxicillin. The baby needed multidisciplinary team approach for surgical repair in future, include; paediatric surgeon, paediatric urologist, paediatric nephrologists and paediatrician.","PeriodicalId":8195,"journal":{"name":"Annals of Clinical and Laboratory Research","volume":"117 1","pages":""},"PeriodicalIF":0.0000,"publicationDate":"2018-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":"1","resultStr":"{\"title\":\"A Case Study of Prune Belly Syndrome with Congenital Vesico-Subumbilical Skin Fistula\",\"authors\":\"A. Abuhamda, E. Mazen\",\"doi\":\"10.21767/2386-5180.100254\",\"DOIUrl\":null,\"url\":null,\"abstract\":\"Prune Belly Syndromes (PBS) usually fatal unless there is a communication between the fetal bladder and the amniotic sac. We report a case of PBS with congenital vesico-subumbilical skin fistula in a Palestinian male neonate. The patient had defect abdominal muscles, wrinkled abdominal skin, cryptorchidism, urethral atresia, vesico-subumbilical skin fistula and normal kidney function. Baby was discharged home in general condition with once daily prophylactic dose of oral amoxicillin. The baby needed multidisciplinary team approach for surgical repair in future, include; paediatric surgeon, paediatric urologist, paediatric nephrologists and paediatrician.\",\"PeriodicalId\":8195,\"journal\":{\"name\":\"Annals of Clinical and Laboratory Research\",\"volume\":\"117 1\",\"pages\":\"\"},\"PeriodicalIF\":0.0000,\"publicationDate\":\"2018-01-01\",\"publicationTypes\":\"Journal Article\",\"fieldsOfStudy\":null,\"isOpenAccess\":false,\"openAccessPdf\":\"\",\"citationCount\":\"1\",\"resultStr\":null,\"platform\":\"Semanticscholar\",\"paperid\":null,\"PeriodicalName\":\"Annals of Clinical and Laboratory Research\",\"FirstCategoryId\":\"1085\",\"ListUrlMain\":\"https://doi.org/10.21767/2386-5180.100254\",\"RegionNum\":0,\"RegionCategory\":null,\"ArticlePicture\":[],\"TitleCN\":null,\"AbstractTextCN\":null,\"PMCID\":null,\"EPubDate\":\"\",\"PubModel\":\"\",\"JCR\":\"\",\"JCRName\":\"\",\"Score\":null,\"Total\":0}","platform":"Semanticscholar","paperid":null,"PeriodicalName":"Annals of Clinical and Laboratory Research","FirstCategoryId":"1085","ListUrlMain":"https://doi.org/10.21767/2386-5180.100254","RegionNum":0,"RegionCategory":null,"ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":null,"EPubDate":"","PubModel":"","JCR":"","JCRName":"","Score":null,"Total":0}
A Case Study of Prune Belly Syndrome with Congenital Vesico-Subumbilical Skin Fistula
Prune Belly Syndromes (PBS) usually fatal unless there is a communication between the fetal bladder and the amniotic sac. We report a case of PBS with congenital vesico-subumbilical skin fistula in a Palestinian male neonate. The patient had defect abdominal muscles, wrinkled abdominal skin, cryptorchidism, urethral atresia, vesico-subumbilical skin fistula and normal kidney function. Baby was discharged home in general condition with once daily prophylactic dose of oral amoxicillin. The baby needed multidisciplinary team approach for surgical repair in future, include; paediatric surgeon, paediatric urologist, paediatric nephrologists and paediatrician.