{"title":"层状鱼鳞癣;与麻醉师的不寻常相识:克服障碍","authors":"Ravichandran Narayanan, S. Patil, Raghuvarathan","doi":"10.4103/2394-6954.227080","DOIUrl":null,"url":null,"abstract":"Lamellar ichthyosis constitutes a distinct group of inherited ichthyosis characterized by excessive scaling and dryness. Abnormalities in epidermal differentiation and metabolism contribute to excessive keratinization, which is a hallmark of this disorder. We present here the successful anesthetic management of a 13-year-old boy with lamellar ichthyosis for the correction of Genu Valgum deformity.","PeriodicalId":17751,"journal":{"name":"Karnataka Anaesthesia Journal","volume":"3 1","pages":"6 - 9"},"PeriodicalIF":0.0000,"publicationDate":"2017-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":"1","resultStr":"{\"title\":\"Lamellar Ichthyosis; An Uncommon Acquaintance with Anesthesiologists: Overcoming Barriers\",\"authors\":\"Ravichandran Narayanan, S. Patil, Raghuvarathan\",\"doi\":\"10.4103/2394-6954.227080\",\"DOIUrl\":null,\"url\":null,\"abstract\":\"Lamellar ichthyosis constitutes a distinct group of inherited ichthyosis characterized by excessive scaling and dryness. Abnormalities in epidermal differentiation and metabolism contribute to excessive keratinization, which is a hallmark of this disorder. We present here the successful anesthetic management of a 13-year-old boy with lamellar ichthyosis for the correction of Genu Valgum deformity.\",\"PeriodicalId\":17751,\"journal\":{\"name\":\"Karnataka Anaesthesia Journal\",\"volume\":\"3 1\",\"pages\":\"6 - 9\"},\"PeriodicalIF\":0.0000,\"publicationDate\":\"2017-01-01\",\"publicationTypes\":\"Journal Article\",\"fieldsOfStudy\":null,\"isOpenAccess\":false,\"openAccessPdf\":\"\",\"citationCount\":\"1\",\"resultStr\":null,\"platform\":\"Semanticscholar\",\"paperid\":null,\"PeriodicalName\":\"Karnataka Anaesthesia Journal\",\"FirstCategoryId\":\"1085\",\"ListUrlMain\":\"https://doi.org/10.4103/2394-6954.227080\",\"RegionNum\":0,\"RegionCategory\":null,\"ArticlePicture\":[],\"TitleCN\":null,\"AbstractTextCN\":null,\"PMCID\":null,\"EPubDate\":\"\",\"PubModel\":\"\",\"JCR\":\"\",\"JCRName\":\"\",\"Score\":null,\"Total\":0}","platform":"Semanticscholar","paperid":null,"PeriodicalName":"Karnataka Anaesthesia Journal","FirstCategoryId":"1085","ListUrlMain":"https://doi.org/10.4103/2394-6954.227080","RegionNum":0,"RegionCategory":null,"ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":null,"EPubDate":"","PubModel":"","JCR":"","JCRName":"","Score":null,"Total":0}
Lamellar Ichthyosis; An Uncommon Acquaintance with Anesthesiologists: Overcoming Barriers
Lamellar ichthyosis constitutes a distinct group of inherited ichthyosis characterized by excessive scaling and dryness. Abnormalities in epidermal differentiation and metabolism contribute to excessive keratinization, which is a hallmark of this disorder. We present here the successful anesthetic management of a 13-year-old boy with lamellar ichthyosis for the correction of Genu Valgum deformity.