34岁男性非阻塞性心尖肥厚性心肌病(RCD代码:III‐2A.1)

Q4 Medicine

Journal of Rare Cardiovascular Diseases Pub Date : 2018-01-05 DOI:10.20418/JRCD.VOL3NO5.296

E. Dziewięcka, P. Rubis, S. Wiśniowska-Śmiałek, K. Holcman, A. Leśniak‑Sobelga, M. Hlawaty, M. Kostkiewicz, P. Podolec

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引用次数: 0

摘要

肥厚性心肌病(HCM)是一种心肌原发疾病，表现为区域性(更常见)或全身性心肌肥大，通常导致功能性心脏损害。我们提出一个34岁的男性根尖HCM的病例，他在超声心动图中因心脏肥厚而被送入心脏科。HCM患者的管理是针对心力衰竭治疗和降低左心室流出道或室内梯度(如果存在)。根据患者计算的5年死亡风险，使用HCM risk - scd计算器评估，评估植入式心律转复除颤器的适应症。JRCD 2017;3 (5): 180-183

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A 34‐year‐old man with non‐obstructive apical hypertrophic cardiomyopathy (RCD code: III‐2A.1)

Hypertrophic cardiomyopathy (HCM) is a primary disease of the myocardium that is defined by the presence of regional (more frequent) or global myocardial hypertrophy, which usually results in functional cardiac impairment. We present a case of a 34-year-old man with apical HCM who was admitted to the cardiology department due to cardiac hypertrophy in the echocardiogram. The management of HCM patients is directed at heart failure treatment and decreasing left ventricular outflow tract or intraventricular gradient, if present. According to the patient’s calculated 5-year mortality risk, assessed using the HCM Risk-SCD Calculator, indications for implantation of an implantable cardioverter defibrillator were evaluated. JRCD 2017; 3 (5): 180–183

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来源期刊

Journal of Rare Cardiovascular Diseases Medicine-Cardiology and Cardiovascular Medicine

自引率

0.00%

发文量

审稿时长

23 weeks

期刊介绍： Journal of Rare Cardiovascular Diseases (JRCD) is an international, quarterly issued, peer-reviewed, open access, online journal that keeps cardiologists and non-cardiologists up-to-date with rare disorders of the heart and vessels. The Journal publishes fine quality review articles, original, basic and clinical sciences research papers, either positive or negative, case reports and articles on public health issues in the field of rare cardiovascular diseases and orphan cardiovascular drugs. Topics of interest include, but are not limited to the following areas: (1) rare diseases of systemic circulation (2) rare diseases of pulmonary circulation (3) rare diseases of the heart (cardiomyopathies) (4) rare congenital cardiovascular diseases (5) rare arrhythmogenic disorders (6) cardiac tumors and cardiovascular diseases in malignancy (7) cardiovascular diseases in pregnancy (8) basic science (9) quality of life