原发性淋巴管瘤、下肢淋巴水肿的胎儿在超声检查中的应用

O. Aksenova, E. Chaplygina, O. Kaplunova, V. G. Bedarev, G. V. Bedarev, O. T. Vartanova
{"title":"原发性淋巴管瘤、下肢淋巴水肿的胎儿在超声检查中的应用","authors":"O. Aksenova, E. Chaplygina, O. Kaplunova, V. G. Bedarev, G. V. Bedarev, O. T. Vartanova","doi":"10.21886/2219-8075-2022-13-3-188-192","DOIUrl":null,"url":null,"abstract":"Scientifically based and experimentally confirmed data on the morphogenesis of the lymphatic system are necessary to clarify critical periods of development characterized by an increased risk of congenital anomalies of the lymphatic system in order to plan and implement effective prevention, diagnosis and correction of related abnormalities. Among the studied anomalies of lymphatic vessels, lymphangioma is most often mentioned — a congenital benign tumor consisting of many cysts of various sizes. Detection of primary fetal lymphangioma in the early stages of intrauterine development is extremely rare. The purpose of the study: to report a case of early diagnosis of congenital cystic lymphangioma and lymphedema of the left lower limb of the fetus. Congenital (primary) peripheral lymphedema, limb lymphangioma is associated with a malformation of the lymphatic system. Taking into account the fact that operative methods of correction of all types of primary lymphedema are considered unreasonable and ineffective, the main attention requires timely detection of this congenital malformation during screening studies of the fetus and the issuance of recommendations for the management of pregnancy, up to termination for medical reasons. It is necessary to raise the issue of genetic counseling of the couple and conducting the necessary genetic studies. The use of modern diagnostic methods allows for the prevention and treatment of abnormalities in the development of the lymphatic system at an earlier stage of the intrauterine period.","PeriodicalId":18314,"journal":{"name":"Medical Herald of the South of Russia","volume":null,"pages":null},"PeriodicalIF":0.0000,"publicationDate":"2022-09-22","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":"0","resultStr":"{\"title\":\"Primary lymphangioma, lymphedema of the lower limb of the fetus in the practice of ultrasound\",\"authors\":\"O. Aksenova, E. Chaplygina, O. Kaplunova, V. G. Bedarev, G. V. Bedarev, O. T. Vartanova\",\"doi\":\"10.21886/2219-8075-2022-13-3-188-192\",\"DOIUrl\":null,\"url\":null,\"abstract\":\"Scientifically based and experimentally confirmed data on the morphogenesis of the lymphatic system are necessary to clarify critical periods of development characterized by an increased risk of congenital anomalies of the lymphatic system in order to plan and implement effective prevention, diagnosis and correction of related abnormalities. Among the studied anomalies of lymphatic vessels, lymphangioma is most often mentioned — a congenital benign tumor consisting of many cysts of various sizes. Detection of primary fetal lymphangioma in the early stages of intrauterine development is extremely rare. The purpose of the study: to report a case of early diagnosis of congenital cystic lymphangioma and lymphedema of the left lower limb of the fetus. Congenital (primary) peripheral lymphedema, limb lymphangioma is associated with a malformation of the lymphatic system. Taking into account the fact that operative methods of correction of all types of primary lymphedema are considered unreasonable and ineffective, the main attention requires timely detection of this congenital malformation during screening studies of the fetus and the issuance of recommendations for the management of pregnancy, up to termination for medical reasons. It is necessary to raise the issue of genetic counseling of the couple and conducting the necessary genetic studies. The use of modern diagnostic methods allows for the prevention and treatment of abnormalities in the development of the lymphatic system at an earlier stage of the intrauterine period.\",\"PeriodicalId\":18314,\"journal\":{\"name\":\"Medical Herald of the South of Russia\",\"volume\":null,\"pages\":null},\"PeriodicalIF\":0.0000,\"publicationDate\":\"2022-09-22\",\"publicationTypes\":\"Journal Article\",\"fieldsOfStudy\":null,\"isOpenAccess\":false,\"openAccessPdf\":\"\",\"citationCount\":\"0\",\"resultStr\":null,\"platform\":\"Semanticscholar\",\"paperid\":null,\"PeriodicalName\":\"Medical Herald of the South of Russia\",\"FirstCategoryId\":\"1085\",\"ListUrlMain\":\"https://doi.org/10.21886/2219-8075-2022-13-3-188-192\",\"RegionNum\":0,\"RegionCategory\":null,\"ArticlePicture\":[],\"TitleCN\":null,\"AbstractTextCN\":null,\"PMCID\":null,\"EPubDate\":\"\",\"PubModel\":\"\",\"JCR\":\"\",\"JCRName\":\"\",\"Score\":null,\"Total\":0}","platform":"Semanticscholar","paperid":null,"PeriodicalName":"Medical Herald of the South of Russia","FirstCategoryId":"1085","ListUrlMain":"https://doi.org/10.21886/2219-8075-2022-13-3-188-192","RegionNum":0,"RegionCategory":null,"ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":null,"EPubDate":"","PubModel":"","JCR":"","JCRName":"","Score":null,"Total":0}
引用次数: 0

摘要

为了规划和实施有效的预防、诊断和纠正相关异常,需要有科学依据和实验证实的淋巴系统形态发生数据,以明确以淋巴系统先天性异常风险增加为特征的发育关键时期。在研究的淋巴管异常中,最常提到的是淋巴管瘤——一种由许多大小不等的囊肿组成的先天性良性肿瘤。在宫内发育早期发现原发性胎儿淋巴管瘤是非常罕见的。本研究的目的:报告1例胎儿左下肢先天性囊性淋巴管瘤及淋巴水肿的早期诊断。先天性(原发性)外周淋巴水肿,肢体淋巴管瘤与淋巴系统畸形有关。考虑到矫正所有类型原发性淋巴水肿的手术方法被认为是不合理和无效的,主要注意的是在对胎儿进行筛查研究期间及时发现这种先天性畸形,并就妊娠管理提出建议,直至因医疗原因终止妊娠。有必要提出对夫妇进行遗传咨询的问题,并进行必要的遗传研究。现代诊断方法的使用允许在宫内早期阶段预防和治疗淋巴系统发育异常。
本文章由计算机程序翻译,如有差异,请以英文原文为准。
Primary lymphangioma, lymphedema of the lower limb of the fetus in the practice of ultrasound
Scientifically based and experimentally confirmed data on the morphogenesis of the lymphatic system are necessary to clarify critical periods of development characterized by an increased risk of congenital anomalies of the lymphatic system in order to plan and implement effective prevention, diagnosis and correction of related abnormalities. Among the studied anomalies of lymphatic vessels, lymphangioma is most often mentioned — a congenital benign tumor consisting of many cysts of various sizes. Detection of primary fetal lymphangioma in the early stages of intrauterine development is extremely rare. The purpose of the study: to report a case of early diagnosis of congenital cystic lymphangioma and lymphedema of the left lower limb of the fetus. Congenital (primary) peripheral lymphedema, limb lymphangioma is associated with a malformation of the lymphatic system. Taking into account the fact that operative methods of correction of all types of primary lymphedema are considered unreasonable and ineffective, the main attention requires timely detection of this congenital malformation during screening studies of the fetus and the issuance of recommendations for the management of pregnancy, up to termination for medical reasons. It is necessary to raise the issue of genetic counseling of the couple and conducting the necessary genetic studies. The use of modern diagnostic methods allows for the prevention and treatment of abnormalities in the development of the lymphatic system at an earlier stage of the intrauterine period.
求助全文
通过发布文献求助,成功后即可免费获取论文全文。 去求助
来源期刊
自引率
0.00%
发文量
0
×
引用
GB/T 7714-2015
复制
MLA
复制
APA
复制
导出至
BibTeX EndNote RefMan NoteFirst NoteExpress
×
提示
您的信息不完整,为了账户安全,请先补充。
现在去补充
×
提示
您因"违规操作"
具体请查看互助需知
我知道了
×
提示
确定
请完成安全验证×
copy
已复制链接
快去分享给好友吧!
我知道了
右上角分享
点击右上角分享
0
联系我们:info@booksci.cn Book学术提供免费学术资源搜索服务,方便国内外学者检索中英文文献。致力于提供最便捷和优质的服务体验。 Copyright © 2023 布克学术 All rights reserved.
京ICP备2023020795号-1
ghs 京公网安备 11010802042870号
Book学术文献互助
Book学术文献互助群
群 号:481959085
Book学术官方微信