A. Szyszkowska, M. Giaro, P. Lisowski, R. Maciąg, A. Lisowska
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引用次数: 0
摘要
May - Thurner综合征是一种罕见的血管疾病,患者的右髂总动脉压迫左髂总静脉。女性的发病率是男性的5倍,通常发生在20多岁和40多岁。患者患有深静脉血栓、血栓后综合征和肺栓塞。他们通常表现为左腿肿胀、慢性腿痛、皮肤颜色改变、受累肢体刺痛和/或麻木、静脉曲张、静脉炎和静脉淤积溃疡。可用的诊断测试包括静脉双工超声、计算机断层扫描、磁共振成像、静脉造影和血管内超声。血管内治疗,包括血管成形术、支架植入和导管定向溶栓是目前的主要治疗方法。长期抗凝和弹性压缩袜用于防止血栓形成和降低血栓后综合征的风险。血栓病筛查是必不可少的,因为它将有助于抗凝治疗继续的决策过程。我们报告了一位38岁的第四次怀孕女性,表现为持续的左腿水肿和复发性深静脉血栓形成,最终被诊断为May - Thurner综合征。JRCD 2018;4(1): 22-25。
May-Thurner Syndrome – Diagnostic and therapeutic dilemmas (RCD code: I-1D.2)
May‐Thurner Syndrome is a rare vascular disease in which the right common iliac artery compresses the left common iliac vein. It occurs 5 times more often in women than in men, usually in their 20s and 40s. Patients suffer from deep vein thrombosis, post‐thrombotic syndrome, and pulmonary embolism. They usually present with swelling of the left leg, chronic leg pain, skin colour changes, tingling and/or numbness of the affected limb, varicosities, phlebitis, and venous stasis ulcers. Available diagnostic tests include venous duplex ultrasound, computed tomography, magnetic resonance imaging, venography, and intravascular ultrasound. Endovascular therapy, including angioplasty, stenting, and catheter‐directed thrombolysis is the current mainstay of treatment. Long‐term anticoagulation and elastic compression stockings are used to prevent recurrent blood clot formation and decrease the risk of post‐thrombotic syndrome. Thrombophilia screening is essential, as it would aid in the decision‐making process regarding continuation of anticoagulant therapy. We present the case of a 38‐year‐old woman in her fourth pregnancy, presenting with persistent left leg oedema and recurrent deep vein thrombosis, eventually diagnosed with May‐Thurner Syndrome. JRCD 2018; 4 (1): 22-25.
期刊介绍:
Journal of Rare Cardiovascular Diseases (JRCD) is an international, quarterly issued, peer-reviewed, open access, online journal that keeps cardiologists and non-cardiologists up-to-date with rare disorders of the heart and vessels. The Journal publishes fine quality review articles, original, basic and clinical sciences research papers, either positive or negative, case reports and articles on public health issues in the field of rare cardiovascular diseases and orphan cardiovascular drugs. Topics of interest include, but are not limited to the following areas: (1) rare diseases of systemic circulation (2) rare diseases of pulmonary circulation (3) rare diseases of the heart (cardiomyopathies) (4) rare congenital cardiovascular diseases (5) rare arrhythmogenic disorders (6) cardiac tumors and cardiovascular diseases in malignancy (7) cardiovascular diseases in pregnancy (8) basic science (9) quality of life