x -连锁少汗性外胚层发育不良治疗与可移动假体在儿科患者。病例报告

Q4 Dentistry

Journal of Oral Research Pub Date : 2022-10-30 DOI:10.17126/joralres.2022.055

H. Rodríguez, José Rodríguez, M. A. de Camargo, Hazel Topel, M. Hirschhaut

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引用次数: 0

摘要

外胚层发育不良是一种罕见的遗传性疾病，影响来自外胚层的结构，如牙齿、头发、指甲和汗腺。少齿症是一种常见的发现，影响这些儿科患者的咀嚼，微笑和自尊。病例报告:我们提出一个病例报告，一个7岁的儿童患者咨询他的母亲，显示相同的条件。干预包括可移动假体，结果令人满意。结论:对于根据颅面发育、年龄、社会经济地位和缺牙数量为患者提供康复治疗的儿科牙医来说，x -联型少汗性外胚层发育不良是一个挑战。

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X-linked hypohidrotic ectodermal dysplasia management with removable prosthesis in a pediatric patient. Case Report

Introduction: Ectodermal dysplasia is a rare genetic disorder that affects structures derived from ectoderm such as teeth, hair, nails, and sweat glands. Oligodontia is a common finding that affects the chewing, smiling and self- esteem of these pediatric patients. Case Report: We present a case report of a 7-years-old pediatric patient who consulted with his mother, showing the same condition. The intervention consisted of a removable prosthesis with satisfactory results. Conclusion: The X-linked hypohidrotic ectodermal dysplasia represents a challenge for a pediatric dentist who offers rehabilitation to the patient according to craniofacial development, age, socioeconomic status, and the number of missing teeth.

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来源期刊

Journal of Oral Research Dentistry-Dentistry (all)

CiteScore

0.50

自引率

0.00%

发文量

审稿时长

8 weeks

期刊介绍： Journal of Oral Research which is published every two month, is devoted to the dissemination of knowledge in oral and craniofacial sciences, including: oral surgery and medicine and rehabilitation, craniofacial surgery, dentistry, orofacial pain and motor disorders, head and neck surgery, speech and swallowing disorders, and other related disciplines. Journal of Oral Research publishes original research articles and brief communications, systematic reviews, study protocols, research hypotheses, reports of cases, comments and perspectives. Indexed by Scopus, DOAJ, LILACS, Latindex, IMBIOMED, DIALNET,REDIB and Google Scholar. Journal of Oral Research is a member of COPE.