{"title":"一例MURCS综合征的麻醉处理","authors":"J. Rekha, Poonam Arora, R. Arora, Monica Arora","doi":"10.4103/aer.aer_137_21","DOIUrl":null,"url":null,"abstract":"MURCS syndrome is a more severe form of Mayer-Rokitansky-Küster-Hauser (MRKH) syndrome, an acronym meaning aplasia/hypoplasia of Müllerian ducts (MU), congenital renal agenesis/ectopia (R), and cervical somite dysplasia (CS). A common presentation is primary amenorrhea in adolescent females. An anesthetist must consider the benefits and limitations of both regional and general anesthesia for these patients based on site of surgery and severity of malformations. We report successful anesthetic management of a 21-year-old female with MURCS syndrome scheduled for a creation of neovagina under spinal anesthesia using ultrasound guidance.","PeriodicalId":7798,"journal":{"name":"Anesthesia, Essays and Researches","volume":"177 1","pages":"454 - 456"},"PeriodicalIF":0.0000,"publicationDate":"2021-10-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":"0","resultStr":"{\"title\":\"Anesthetic Management in a Case of MURCS Syndrome\",\"authors\":\"J. Rekha, Poonam Arora, R. Arora, Monica Arora\",\"doi\":\"10.4103/aer.aer_137_21\",\"DOIUrl\":null,\"url\":null,\"abstract\":\"MURCS syndrome is a more severe form of Mayer-Rokitansky-Küster-Hauser (MRKH) syndrome, an acronym meaning aplasia/hypoplasia of Müllerian ducts (MU), congenital renal agenesis/ectopia (R), and cervical somite dysplasia (CS). A common presentation is primary amenorrhea in adolescent females. An anesthetist must consider the benefits and limitations of both regional and general anesthesia for these patients based on site of surgery and severity of malformations. We report successful anesthetic management of a 21-year-old female with MURCS syndrome scheduled for a creation of neovagina under spinal anesthesia using ultrasound guidance.\",\"PeriodicalId\":7798,\"journal\":{\"name\":\"Anesthesia, Essays and Researches\",\"volume\":\"177 1\",\"pages\":\"454 - 456\"},\"PeriodicalIF\":0.0000,\"publicationDate\":\"2021-10-01\",\"publicationTypes\":\"Journal Article\",\"fieldsOfStudy\":null,\"isOpenAccess\":false,\"openAccessPdf\":\"\",\"citationCount\":\"0\",\"resultStr\":null,\"platform\":\"Semanticscholar\",\"paperid\":null,\"PeriodicalName\":\"Anesthesia, Essays and Researches\",\"FirstCategoryId\":\"1085\",\"ListUrlMain\":\"https://doi.org/10.4103/aer.aer_137_21\",\"RegionNum\":0,\"RegionCategory\":null,\"ArticlePicture\":[],\"TitleCN\":null,\"AbstractTextCN\":null,\"PMCID\":null,\"EPubDate\":\"\",\"PubModel\":\"\",\"JCR\":\"\",\"JCRName\":\"\",\"Score\":null,\"Total\":0}","platform":"Semanticscholar","paperid":null,"PeriodicalName":"Anesthesia, Essays and Researches","FirstCategoryId":"1085","ListUrlMain":"https://doi.org/10.4103/aer.aer_137_21","RegionNum":0,"RegionCategory":null,"ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":null,"EPubDate":"","PubModel":"","JCR":"","JCRName":"","Score":null,"Total":0}
引用次数: 0
摘要
MURCS综合征是一种更为严重的mayer - rokitansky - k ster- hauser (MRKH)综合征，MRKH是一个缩写，意思是勒氏管发育不全/发育不全(MU)、先天性肾发育不全/异位(R)和宫颈体发育不良(CS)。青春期女性原发性闭经是一种常见的表现。麻醉师必须根据手术部位和畸形的严重程度考虑局部麻醉和全身麻醉对这些患者的益处和局限性。我们报告一位21岁女性MURCS综合征患者在超声引导下脊髓麻醉下新阴道的成功麻醉处理。
MURCS syndrome is a more severe form of Mayer-Rokitansky-Küster-Hauser (MRKH) syndrome, an acronym meaning aplasia/hypoplasia of Müllerian ducts (MU), congenital renal agenesis/ectopia (R), and cervical somite dysplasia (CS). A common presentation is primary amenorrhea in adolescent females. An anesthetist must consider the benefits and limitations of both regional and general anesthesia for these patients based on site of surgery and severity of malformations. We report successful anesthetic management of a 21-year-old female with MURCS syndrome scheduled for a creation of neovagina under spinal anesthesia using ultrasound guidance.
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