壁脓肿显示髓外造血的几个病灶:1例报告

Y. Gharbi
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引用次数: 0

摘要

在儿童中,髓外造血(EMH)是对严重慢性贫血的代偿反应,特别是在B型地中海贫血的情况下。它的定位是可变的,主要是肝脏、脾脏和神经节,但所有其他器官,包括皮肤,都可以到达。罕见的,大多数情况下无症状,EMH可表现为肿块综合征。记忆和影像学带来有利于诊断的争论,有时难以建立,不诉诸侵入性检查。由于治疗的进步,手术治疗已经变得罕见,保留在某些特殊情况下。我们报告的情况下,患者与严重B型地中海贫血,在一个脓肿的腹部肿块的外观已经揭示了几个灶EMH。
本文章由计算机程序翻译,如有差异,请以英文原文为准。
Parietal Abcess Revealing Several Foci of Extramedullary Hematopoiesis: A Case Report
In children, Extra Medullary Hematopoiesis (EMH) is a compensatory response to severe chronic anemia, particularly in the context of B thalassemia. Its localization, variable, is mainly hepatic, splenic and ganglionic but all the other organs, including the skin, can be reached. Rare, most often asymptomatic, EMH can be manifested by a mass syndrome. The anamnesis and the imaging bring arguments in favor of the diagnosis, sometimes difficult to establish, without resorting to invasive examinations. Thanks to therapeutic progress, the surgical treatment has become rare, reserved for certain special cases. We report the case of a patient with major B thalassemia, in whom the appearance of an abscessed abdominal mass has revealed several foci of EMH.
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