L. E. Mangamba, A. Balkissou, V. T. Essoh, AD Batchom, B. Barche, JP Engbang Ndamba, BH Mbatchou Ngahane
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引用次数: 0
摘要
Von Recklinghausen病也被称为1型神经纤维瘤病(NF1),是最常见的遗传性疾病之一。它是神经鞘神经纤维瘤和非常典型的皮肤病变发展的原因。根据文献,胸部损伤是罕见的。自发性血胸是血胸的一个亚类,在没有外伤或其他原因的情况下,血液在胸膜间隙积聚。这种继发于血管受累的临床实体在文献中很少被描述。
Spontaneous Hemothorax of Tumoral Origin Complicating a Von Recklinghausen's Disease: Report of Two Cases in Cameroon and Litterature Review
Von Recklinghausen's disease also known as neurofibromatosis type 1 (NF1), is one of the most common genetic diseases. It is responsible of the development of neurofibromas from nerve sheaths and very typical skin lesions. Chest damage according to the literature is rare. Spontaneous hemothorax is a subcategory of hemothorax that involves the accumulation of blood in the pleural space in the absence of trauma or other causes. This clinical entity secondary to vascular involvement is rarely described in the literature.